cerebruli dambla
Transcrição
cerebruli dambla klinikuri mdgomareobis marTvis saxelmwifo standarti (protokoli) 1 cerebruli dambla (sareabilitacio centri) 1. daavadebis definicia cerebruli dambla aris heterogenuri jgufi klinikuri romlebic xasiaTdeba anomaluri motoruli (moZraobiTi) posturaluri meqanizmebiT. sindromebisa, aqtebiTa da 2. simptomebi da niSnebi ZiriTadi damaxasiaTebeli niSnebia: spastiuroba, moZraobis darRvevebi, kunTTa sisuste, ataqsia, rigiduloba, sirTuleebi yoveldRiuri cxovrebiseuli aqtivobebis ganxorcielebaSi. cerebrul damblasTan asocirebuli darRvevebi motoruli disfunqciis garda TiTqmis yovelTvis moicavs cerebruli funqciis sxva darRvevebs, maT Soris, kognitur (SemecnebiT), mxedvelobis, smenis, metyvelebis, qerquli mgrZnobelobis, yuradRebis, qcevis darRvevebs, epilefsias. daaxloebiT 65%-s cerebruli damblis mTeli populaciisa, aReniSneba sxvadasxva xarisxis mentaluri retardacia da swavlis siZneleebi. 3. diagnostikur – laboratoriuli testebi cerebruli damblis diagnostika saWiroebs Semdeg RonisZiebebs: • pacientis istoriis sruli kvleva – gestaciisa da perinataluri movlenebis detaluri aRricxva; ganviTarebis etapebis dokumentaciuri asaxva. • fizikuri gasinjva – pozis, aqtiur da pasiur moZraobaTa sifarTis, mgrZnobelobis, Zalis, kunTTa tonusis (spastiurobis), moZraobaTa darRvevis tipisa da xarisxis, kidurebis deformaciebis Sefaseba. damatebiTi gamokvlevebi: • kraniuli ultrasonografia (saWiroebis diagnostikisa da prognozisaTvis); • magnitur-rezonansuli gamosaxva (saWiroebis SemTxvevaSi – adreuli diagnostikis, prognozis, rTulad sadiagnostiko SemTxvevebisa da diferenciuli diagnostikisaTvis); • kompiuteruli tomografia (saWiroebis SemTxvevaSi – adreuli diagnostikis, prognozis, rTulad sadiagnostiko SemTxvevebisa da diferenciuli diagnostikisaTvis); • eleqtroencefalografia (saWiroebis SemTxvevaSi); SemTxvevaSi – adreuli 2 • genetikuri kvleva (saWiroebis SemTxvevaSi – metabolizmis Tandayolil defeqtebze da sxva genetikur darRvevebze, diferenciuli diagnostikisaTvis). Sefasebis instrumentebi: • globaluri funqciis Sefaseba – "funqciuri damoukideblobis sazomi bavSvebisaTvis" (WeeFIM – Functional Independence Measure for Children); • msxvili motoruli funqciis Sefaseba – "msxvili motoruli funqciis sazomi" (GMFM – Gross Motor Function Measure); • spastiurobis gazomva da analizi – "aSuorTis spastiurobis Skala" (Ashworth Spasticity Scale); • simZimis Sefaseba – "cerebruli damblis simZimis rusmanis da geijis Skala" (Severity of Cerebral Palsy by Russman and Gage); • janmrTelobasTan dakavSirebuli sicocxlis xarisxis Sefaseba "bavSvis janmrTelobis kiTxvari" (CHQ – Child Health Questionnaire). • kognituri unarebisa da gonebrivi ganviTarebis Sefaseba (saWiroebis SemTxvevaSi), sxvadasxva asakobrivi jgufebisaTvis – "Cvili bavSvis ganviTarebis beilis Skala" (Bayley Scales of Infant Development); "kaufmanis batarea bavSvis SefasebisaTvis" (Kaufmann Assessment Battery for Children); "veqsleris inteleqtis Skala bavSvebisaTvis" (Wechsler Intelligence Scale for Children). (rekomendaciis xarisxi B). – 4. mkurnaloba (marTva) ZiriTadi principi – multi(inter)disciplinuri, gunduri midgoma. a) Terapiuli intervencia – • fizikur Terapia; • okupaciuri Terapia; • metyvelebis da enis Terapia; • fsiqologiuri koreqcia (saWiroebis SemTxvevaSi) b) farmakologiuri (medikamenturi) Terapia – • botulinis neirotoqsinis Semcveli medikamentebi (saWiroebis SemTxvevaSi); • antiepilefsiuri farmakoTerapia (saWiroebis SemTxvevaSi). g) orTopediuli qirurgia – saWiroebis SemTxvevaSi; d) damxmare (teqnologiuri) saSualebebi – • orTezireba (saWiroebis SemTxvevaSi); • gadaadgilebis, dgomis, jdomis, komunikaciisa da garemosTan adaptaciisTvis saWiro damxmare saSualebebis gamoyenebis swavleba. e) mSobelTa an ZiriTad meurveTa ganaTleba da treningi movlisa da Terapiis sakiTxebze. 3 dakvirveba cerebruli dambliT daavadebuli bavSvis sareabilitacio mkurnaloba xangrZlivi da sistematuria. saSualod yovel 6-12 TveSi saWiroa etapuri Sefaseba miznebisa da reabilitaciis programis gadafasebisaTvis. mkurnalobis xangrZlivoba, sixSire da dasruleba ganisazRvreba individualurad calkeuli bavSvisaTvis, profesionalTa multidisciplinuri gundis mier. ZiriTad samiznes warmoadgens ganviTareba, funqciis optimizacia da masTan dakavSirebuli klinikuri maxasiaTeblebi. 5. gaidlaini, romelsac eyrdnoba aRniSnuli protokoli _ “cerebruli dambla” 6. adamianuri da materialur-teqnikuri resursi materialur-teqnikuri resursi – sareabilitacio aRWurviloba; gadaadgilebis, dgomis, jdomis, komunikaciisa da garemosTan adaptaciisTvis saWiro damxmare saSualebebi; SefasebisTvis saWiro testebi da Skalebi. adamianuri resursi – bavSvTa nevrologi an reabilitologi; fizikuri Terapevti; okupaciuri Terapevti; metyvelebisa da enis Terapevti; fsiqologi; orTezisti; eqTani-koordinatori. 4 cerebruli damblis marTvis algoriTmi damaxasiaTebuli niSnebi: spastiuroba, moZraobis darRvevebi, kunTTa sisuste, ataqsia, rigiduloba, moZraobis, wonasworobisa da pozis darRveva, sirTuleebi yoveldRiuri cxovrebiseuli aqtivobebis ganxorcielebaSi. asocirebuli darRvevebi: kognituri (SemecnebiTi), mxedvelobis, smenis, metyvelebis, qerquli mgrZnobelobis, yuradRebis, qcevis darRvevebi; epilefsia; mentaluri retardacia; swavlis siZneleebi. diagnozi Ddiferenciuli diagnozi: • • • • • • • neirodegeneraciuli daaavadebebi; metabolizmis Tandayolili defeqtebi; zurgis tvinis ganviTarebiTi an dazianebebi; nerv-kunTovani daavadebebi; neoplazma; progresirebadi hidrocefalia; subduruli hematoma. pacientis istoriis sruli kvleva: • gestaciisa da perinataluri periodi; • ganviTarebis etapebis dokumentacia; fizikuri gasinjva: • pozis, aqtiuri da pasiuri moZraobis sifarTe; • mgrZnobelobis, Zalis, kunTTa tonusis Sefaseba; • moZraobaTa darRvevis tipisa da xarisxis, kidurebis deformaciis Sefaseba travmuli damatebiTi gamokvlevebi: • kraniuli ultrasonografia*; • magnitur-rezonansuli gamosaxva*; • kompiuteruli tomografia*; • eleqtroencefalografia*; • genetikuri kvleva*. multidisciplinuri gasinjva da Sefaseba bavSvTa nevrologi –gasinjva, diagnozi Sefasebis instrumentebi: • fizikuri Terapevti – gasinjva, problemaTa identificireba • okupaciuri Terapevti –gasinjva, problemaTa identificireba • • • metyvelebisa da enis Terapevti – gasinjva, problemaTa identificireba • • fsiqologi* – problemaTa identificireba • "funqciuri damoukideblobis sazomi bavSvebisaTvis" (WeeFIM – Functional Independence Measure for Children); "msxvili motoruli funqciis sazomi" (GMFM – Gross Motor Function Measure) : "aSuorTis spastiurobis Skala" (Ashworth Spasticity Scale) "cerebruli damblis simZimis rusmanis da geijis Skala" (Severity of Cerebral Palsy by Russman and Gage) "bavSvis janmrTelobis kiTxvari" (CHQ – Child Health Questionnaire); "Cvili bavSvis ganviTarebis beilis Skala" (Bayley Scales of Infant Development)*; "kaufmanis batarea bavSvis SefasebisaTvis" (Kaufmann Assessment Battery for Children)*; "veqsleris inteleqtis Skala bavSvebisaTvis" (Wechsler Intelligence Scale for Children)*. orTezisti* – gasinjva, problemaTa identificireba mkurnalobis mTavari (saboloo) da Sualeduri mimiznebis dasaxva mkurnaloba (menejmenti) fizikuri Terapia orTezireba* botulinis toqsini* okupaciuri Terapia damxmare saSualebebis antiepilefsiuri farmakoTerapia* gamoyenebis swavleba metyvelebis da enis Terapia orTopediuli qirurgia* fsiqologiuri koreqcia* sa mSobelTa instruqtaJi da treningi * saWiroebis SemTxvevaSi (ix. protokoli da gaidlaini). 5
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